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Table 2 Diagnosis and follow up of TART in male patients with congenital adrenal hyperplasia.

From: Testicular Adrenal Rest Tumours in Congenital Adrenal Hyperplasia

(i) Scrotal ultrasound 1 x/year from 8 years onwards

(ii) Biochemical analysis 1 x/year:

   (1) Hormonal control: ACTH, renin, 17-hydroxyprogesterone, androstenedione

   (2) Gonadal function: LH, FSH, inhibin B

(iii) Semen analysis in pubertal and adult patients

(iv) Cryopreservation of semen

(v) When considering surgery: testicular biopsy