Total number of cases 130 | IGHD | MPHD* | |
---|---|---|---|
48/130 (37 %) | 82/130 (63 %) | ||
Congenital n (%) (A,B,C,D) | 38/130 (29 %) | 12 (8,1,2,1) | 26 (14,3,4,5) |
-Pituitary axial structural abnormalities (A,B,C,D) | 24 | 9 (6,1,1,1) | 15 (6,3,1,5) |
-Midline axial structure defects (SOD) (A,B,C,D) | 14 | 3 (2,0,1,0) | 11 (8,0,3,0) |
Oncology/cranial irradiation n (%) (A,B,C,D) | 51/130 (40 %) | 8 (5,3,0,0) | 43 (18,19,4,2) |
- Craniopharyngioma (A,B,C,D) | 15 | – | 15 (6,7,1,1) |
- Hematologic malignancies (A,B,C,D) | 12 | 4 (4,0,0,0) | 8 (6,0,1,1) |
- Medulloblastoma (A,B,C,D) | 6 | 1 (0,1,0,0) | 5 (1,4,0,0) |
- Other CNS tumors (A,B,C,D) | 18 | 3 (1,2,0,0) | 15 (5,8,2,0) |
Idiopathica n (%) (A,B,C,D) | 15/130 (11 %) | 13 (7,1,5,0) | 2 (1,1,0,0) |
Othersb n (%) (A,B,C,D) | 26/130 (20 %) | 15 (12,1,1,1) | 11 (5,3,2,1) |
-Crohn's disease (A,B,C,D) | 4 | 4 (3,0,0,1) | – |
-Coeliac disease (A,B,C,D) | 2 | – | 2 (0,1,1,0) |
-Haematological diseasesc (A,B,C,D) | 2 | 1 (1,0,0,0) | 1 (1,0,0,0) |
-Other diseasesd (A,B,C,D) | 11 | 8 (6,1,1,0) | 3 (0,2,1,0) |
-Syndromese(A,B,C,D) | 6 | 2 (2,0,0,0) | 4 (3,0,0,1) |
-Acquired brain injury (A,B,C,D) | 1 | – | 1 (1,0,0,0) |