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Table 1 Prevalence of NCAH due to 21-hydroxylase deficiency among hyperandrogenic women.

From: Nonclassic Congenital Adrenal Hyperplasia

Country

Total # of Women

# NCAH (%)

Citation

USA (NE)

22*

2 (9%)

Emans et al., 1983 [8]

USA (NE)

139

2 (1.4%)

Cobin et al., 1985 [9]

USA (NE)

164

4 (2.4%)

Azziz and Zacur, 1989 [10]

USA (SE)

86

2 (2.3%)

Azziz et al., 1993 [11]

USA (SW)

83

1 (1.2%)

Chetkowski et al., 1984 [12]

USA (SE)

873

18 (1.6%)

Azziz et al., 2004 [13]

Canada

72

4 (5.5%)

Innanen and Vale, 1990 [14]

Puerto Rico

100

1 (1.0%)

Romaguera et al., 2000 [15]

Ireland

96

6 (6.2%)

McLaughlin et al., 1990 [16]

England

50

1 (2.0%)

Turner et al., 1992 [17]

France

400

24 (6.0%)

Kuttenn et al., 1985 [18]

France

69

16 (23%)

Blanch et al., 1997 [19]

Portugal

129

23 (17.8%)

Pall et al., (in press) [20]

Italy (South)

372

14 (4.0%)

Carmina et al., 1987 [21]

Italy (North)

85

1 (1.1%)

Motta et al., 1988 [22]

Italy (Palermo)

950

41 (4.5%)

Carmina et al., 2006 [23]

Spain

270

6 (2.2%)

Escobar-Morreale et al., 2008 [24]

Czech Republic

298

8 (2.7%)

Fanta et al., 2008 [25]

Greece

107

10 (9.3%)

Trakakis et al., 2008 [26]

Turkey (Ankara)

32*

1(3%)

Akinci et al., 1992 [27]

Turkey (Istanbul)

61

20 (33%)

Yarman et al., 2004 [28]

Turkey (Kayseri)

285

6 (2.1%)

Unluhizarci et al., 2010 [29]

Turkey (Central Anatolia)

63

6 (9.5%)

Kamel et al., 2003 [30]

Israel

170

14 (8.2%)

Eldar-Geva et al., 1990 [31]

India

60

3 (8.3%)

Mithal et al., 1988 [32]

India

63

3 (5.7%)

Khandekar et al., 1990 [33]

  1. *adolescent girls.